Pulmonary hypertension in familial Mediterranean fever: consequence or coincidence?
نویسندگان
چکیده
Objectives FMF is the most common autoinflammatory disease characterized by recurrent febrile polyserositis. The gravest consequence of FMF is nephropatic amyloidosis of AA type, which may progress to affect other organs, including the lungs[]. Pulmonary hypertension (PH) in FMF related amyloidosis is rare; only a few cases have been reported so far[,]. We aim to elucidate development of PH in FMF in Armenian patients group.
منابع مشابه
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عنوان ژورنال:
دوره 13 شماره
صفحات -
تاریخ انتشار 2015